E71: Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E71.3: Disorders of fatty-acid metabolism

excludes1
peroxisomal disorders (E71.5)
Refsum's disease (G60.1)
Schilder's disease (G37.0)

excludes2
carnitine deficiency due to inborn error of metabolism (E71.42)
E71.30: Disorder of fatty-acid metabolism, unspecified
E71.31: Disorders of fatty-acid oxidation
E71.32: Disorders of ketone metabolism
E71.39: Other disorders of fatty-acid metabolism

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