Metabolic disorders (E70-E88)
E75: Disorders of sphingolipid metabolism and other lipid storage disorders

excludes1
mucolipidosis, types I-III (E77.0-E77.1)
Refsum's disease (G60.1)
E75.0: GM2 gangliosidosis
E75.1: Other and unspecified gangliosidosis
E75.2: Other sphingolipidosis
E75.3: Sphingolipidosis, unspecified
E75.4: Neuronal ceroid lipofuscinosis
E75.5: Other lipid storage disorders
E75.6: Lipid storage disorder, unspecified

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