E75.2: Other sphingolipidosis
E75.24: Niemann-Pick disease

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Acid sphingomyelinase deficiency (ASMD)

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Acid sphingomyelinase deficiency type A (ASMD type A)
Infantile neurovisceral acid sphingomyelinase deficiency

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Acid sphingomyelinase deficiency type B (ASMD type B)
Chronic visceral acid sphingomyelinase deficiency

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Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
Chronic neurovisceral acid sphingomyelinase deficiency

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Acid sphingomyelinase deficiency (ASMD) NOS
E75.240: Niemann-Pick disease type A
E75.241: Niemann-Pick disease type B
E75.242: Niemann-Pick disease type C
E75.243: Niemann-Pick disease type D
E75.244: Niemann-Pick disease type A/B
E75.248: Other Niemann-Pick disease
E75.249: Niemann-Pick disease, unspecified

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