I27: Other pulmonary heart diseases
I27.0: Primary pulmonary hypertension

inclusionTerm
Heritable pulmonary arterial hypertension
Idiopathic pulmonary arterial hypertension
Primary group 1 pulmonary hypertension
Primary pulmonary arterial hypertension

excludes1
persistent pulmonary hypertension of newborn (P29.30)
pulmonary hypertension NOS (I27.20)
secondary pulmonary arterial hypertension (I27.21)
secondary pulmonary hypertension (I27.29)

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