D56: Thalassemia
D56.0: Alpha thalassemia

inclusionTerm
Alpha thalassemia major
Hemoglobin H Constant Spring
Hemoglobin H disease
Hydrops fetalis due to alpha thalassemia
Severe alpha thalassemia
Triple gene defect alpha thalassemia

useAdditionalCode
code, if applicable, for hydrops fetalis due to alpha thalassemia (P56.99)

excludes1
alpha thalassemia trait or minor (D56.3)
asymptomatic alpha thalassemia (D56.3)
hydrops fetalis due to isoimmunization (P56.0)
hydrops fetalis not due to immune hemolysis (P83.2)

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