Certain disorders involving the immune mechanism (D80-D89)
D81: Combined immunodeficiencies

excludes1
autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
D81.0: Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1: Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2: Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3: Adenosine deaminase [ADA] deficiency
D81.4: Nezelof's syndrome
D81.5: Purine nucleoside phosphorylase [PNP] deficiency
D81.6: Major histocompatibility complex class I deficiency
D81.7: Major histocompatibility complex class II deficiency
D81.8: Other combined immunodeficiencies
D81.9: Combined immunodeficiency, unspecified

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