D89.4: Mast cell activation syndrome and related disorders excludes1 aggressive systemic mastocytosis (C96.21) congenital cutaneous mastocytosis (Q82.2) (non-congenital) cutaneous mastocytosis (D47.01) (indolent) systemic mastocytosis (D47.02) malignant mast cell neoplasm (C96.2-) malignant mastocytoma (C96.29) mast cell leukemia (C94.3-) mast cell sarcoma (C96.22) mastocytoma NOS (D47.09) other mast cell neoplasms of uncertain behavior (D47.09) systemic mastocytosis associated with a clonal hematologic non-mast cell lineage disease (SM-AHNMD) (D47.02) |
| D89.40: Mast cell activation, unspecified |
| D89.41: Monoclonal mast cell activation syndrome |
| D89.42: Idiopathic mast cell activation syndrome |
| D89.43: Secondary mast cell activation |
| D89.44: Hereditary alpha tryptasemia |
| D89.49: Other mast cell activation disorder |