ARTHROPATHIES AND RELATED DISORDERS (710-719)
Excludes:
disorders of spine (720.0-724.9)
710 Diffuse diseases of connective tissue
Includes:
all collagen diseases whose effects are not mainly confined to a single system
Excludes:
those affecting mainly the cardiovascular system, i.e., polyarteritis nodosa and allied conditions (446.0-446.7)
Disseminated lupus erythematosus
Libman-Sacks disease
Use additional code to identify manifestation, as:
endocarditis (424.91)
nephritis (583.81)
chronic (582.81)
nephrotic syndrome (581.81)
Excludes:
lupus erythematosus (discoid) NOS (695.4)
Acrosclerosis
CRST syndrome
Progressive systemic sclerosis
Scleroderma
Use additional code to identify manifestation, as:
lung involvement (517.2)
myopathy (359.6)
Excludes:
circumscribed scleroderma (701.0)
Keratoconjunctivitis sicca
Sjögren's disease
Poikilodermatomyositis
Polymyositis with skin involvement
Toxic oil syndrome
Use additional E to identify drug, if drug induced
Multifocal fibrosclerosis (idiopathic) NEC
Systemic fibrosclerosing syndrome

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