209: Neuroendocrine tumors
Code first any associated multiple endocrine neoplasia syndrome (258.01-258.03)
Use additional code to identify associated endocrine syndrome, such as:
carcinoid syndrome (259.2)
Excludes:
benign pancreatic islet cell tumors (211.7)
malignant pancreatic islet cell tumors (157.4)
209.7 Secondary neuroendocrine tumors
Secondary carcinoid tumors
Mesentery metastasis of neuroendocrine tumor
Merkel cell carcinoma nodal presentation
Merkel cell carcinoma visceral metastatic presentation
Secondary Merkel cell carcinoma, any site

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