ICD-9-CM

Use additional code to identify any associated intellectual disabilities

271 Disorders of carbohydrate transport and metabolism Excludes: abnormality of secretion of glucagon (251.4) diabetes mellitus (249.0-249.9, 250.0-250.9) hypoglycemia NOS (251.2) mucopolysaccharidosis (277.5)
271.0: Glycogenosis Amylopectinosis Glucose-6-phosphatase deficiency Glycogen storage disease McArdle's disease Pompe's disease von Gierke's disease
271.1: Galactosemia Galactose-1-phosphate uridyl transferase deficiency Galactosuria
271.2: Hereditary fructose intolerance Essential benign fructosuria Fructosemia
271.3: Intestinal disaccharidase deficiencies and disaccharide malabsorption Intolerance or malabsorption (congenital) (of): glucose-galactose lactose sucrose-isomaltose
271.4: Renal glycosuria Renal diabetes
271.8: Other specified disorders of carbohydrate transport and metabolism Essential benign pentosuria Fucosidosis Glycolic aciduria Hyperoxaluria (primary) Mannosidosis Oxalosis Xylosuria Xylulosuria
271.9: Unspecified disorder of carbohydrate transport and metabolism

271 Disorders of carbohydrate transport and metabolism

Excludes:

abnormality of secretion of glucagon (251.4)

diabetes mellitus (249.0-249.9, 250.0-250.9)

hypoglycemia NOS (251.2)

mucopolysaccharidosis (277.5)

Amylopectinosis

Glucose-6-phosphatase deficiency

Glycogen storage disease

McArdle's disease

Pompe's disease