OTHER METABOLIC AND IMMUNITY DISORDERS (270-279)
Use additional code to identify any associated intellectual disabilities
273 Disorders of plasma protein metabolism
Excludes:
agammaglobulinemia and hypogammaglobulinemia (279.0-279.2)
coagulation defects (286.0-286.9)
hereditary hemolytic anemias (282.0-282.9)
273.0: Polyclonal hypergammaglobulinemia
Hypergammaglobulinemic purpura:
benign primary
Waldenström's
273.1: Monoclonal paraproteinemia
Benign monoclonal hypergammaglobulinemia [BMH]
Monoclonal gammopathy:
NOS
associated with lymphoplasmacytic dyscrasias
benign
Paraproteinemia:
benign (familial)
secondary to malignant or inflammatory disease
273.2: Other paraproteinemias
Cryoglobulinemic:
purpura
vasculitis
Mixed cryoglobulinemia
273.3: Macroglobulinemia
Macroglobulinemia (idiopathic) (primary)
Waldenström's macroglobulinemia
273.4: Alpha-1-antitrypsin deficiency
AAT deficiency
273.8: Other disorders of plasma protein metabolism
Abnormality of transport protein
Bisalbuminemia
273.9: Unspecified disorder of plasma protein metabolism
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