277: Other and unspecified disorders of metabolism
277.0 Cystic fibrosis
Fibrocystic disease of the pancreas
Mucoviscidosis
277.00: Without mention of meconium ileus
Cystic fibrosis NOS
277.01: With meconium ileus
Meconium:
ileus (of newborn)
obstruction of intestine in mucoviscidosis
277.02: With pulmonary manifestations
Cystic fibrosis with pulmonary exacerbation
Use additional code to identify any infectious organism present, such as:
pseudomonas (041.7)
277.03: With gastrointestinal manifestations
Excludes:
with meconium ileus (277.01)
277.09: With other manifestations
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