277: Other and unspecified disorders of metabolism
277.0 Cystic fibrosis
Fibrocystic disease of the pancreas
Mucoviscidosis
Meconium:
ileus (of newborn)
obstruction of intestine in mucoviscidosis
Cystic fibrosis with pulmonary exacerbation
Use additional code to identify any infectious organism present, such as:
pseudomonas (041.7)
Excludes:
with meconium ileus (277.01)

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