OTHER METABOLIC AND IMMUNITY DISORDERS (270-279)
Use additional code to identify any associated intellectual disabilities
279 Disorders involving the immune mechanism
Use additional code for associated manifestations
Agammaglobulinemia:
autosomal recessive
Swiss-type
X-linked recessive
Severe combined immunodeficiency [SCID]
Thymic:
alymphoplasia
aplasia or dysplasia with immunodeficiency
Excludes:
thymic hypoplasia (279.11)
Excludes:
transplant failure or rejection (996.80-996.89)
Code first underlying cause, such as:
complication of blood transfusion (999.89)
complication of transplanted organ (996.80-996.89)
Use additional code to identify associated manifestations, such as:
desquamative dermatitis (695.89)
diarrhea (787.91)
elevated bilirubin (782.4)
hair loss (704.09)
Single complement [C1-C9] deficiency or dysfunction

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