4. DISEASES OF THE BLOOD AND BLOOD-FORMING ORGANS (280-289)
282 Hereditary hemolytic anemias
282.0: Hereditary spherocytosis
Acholuric (familial) jaundice
Congenital hemolytic anemia (spherocytic)
Congenital spherocytosis
Minkowski-Chauffard syndrome
Spherocytosis (familial)
Excludes:
hemolytic anemia of newborn (773.0-773.5)
282.1: Hereditary elliptocytosis
Elliptocytosis (congenital)
Ovalocytosis (congenital) (hereditary)
282.2: Anemias due to disorders of glutathione metabolism
Anemia:
6-phosphogluconic dehydrogenase deficiency
enzyme deficiency, drug-induced
erythrocytic glutathione deficiency
glucose-6-phosphate dehydrogenase [G-6-PD] deficiency
glutathione-reductase deficiency
hemolytic nonspherocytic (hereditary), type I
Disorder of pentose phosphate pathway
Favism
282.3: Other hemolytic anemias due to enzyme deficiency
Anemia:
hemolytic nonspherocytic (hereditary), type II
hexokinase deficiency
pyruvate kinase [PK] deficiency
triosephosphate isomerase deficiency
282.4: Thalassemias
Excludes:
sickle-cell:
disease (282.60-282.69)
trait (282.5)
282.5: Sickle-cell trait
Hb-AS genotype
Hemoglobin S [Hb-S] trait
Heterozygous:
hemoglobin S
Hb-S
Excludes:
that with other hemoglobinopathy (282.60-282.69)
that with thalassemia (282.41-282.42)
282.6: Sickle-cell disease
Sickle-cell anemia
Excludes:
sickle-cell thalassemia (282.41-282.42)
sickle-cell trait (282.5)
282.7: Other hemoglobinopathies
Abnormal hemoglobin NOS
Congenital Heinz-body anemia
Disease:
hemoglobin C [Hb-C]
hemoglobin D [Hb-D]
hemoglobin E [Hb-E]
hemoglobin Zurich [Hb-Zurich]
Hemoglobinopathy NOS
Hereditary persistence of fetal hemoglobin [HPFH]
Unstable hemoglobin hemolytic disease
Excludes:
familial polycythemia (289.6)
hemoglobin E-beta thalassemia (282.47)
hemoglobin M [Hb-M] disease (289.7)
high-oxygen-affinity hemoglobin (289.0)
other hemoglobinopathies with thalassemia (282.49)
282.8: Other specified hereditary hemolytic anemias
Stomatocytosis
282.9: Hereditary hemolytic anemia, unspecified
Hereditary hemolytic anemia NOS

Home