282.6: Sickle-cell disease
Sickle-cell anemia
Excludes:
sickle-cell thalassemia (282.41-282.42)
sickle-cell trait (282.5)
282.64 Sickle-cell/HB-C disease with crisis
Hb-S/Hb-C disease with crisis
Sickle-cell/Hb-C disease with vaso-occlusive pain
Use additional code for types of crisis, such as:
Acute chest syndrome (517.3)
Splenic sequestration (289.52)

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