046: Slow virus infections and prion diseases of central nervous system
046.1 Jakob-Creutzfeldt disease
Use additional code to identify dementia:
with behavioral disturbance (294.11)
without behavioral disturbance (294.10)
046.11: Variant Creutzfeldt-Jakob disease
vCJD
046.19: Other and unspecified Creutzfeldt-Jakob disease
CJD
Familial Creutzfeldt-Jakob disease
Iatrogenic Creutzfeldt-Jakob disease
Jakob-Creutzfeldt disease, unspecified
Sporadic Creutzfeldt-Jakob disease
Subacute spongiform encephalopathy
Excludes:
variant Creutzfeldt-Jakob disease (vCJD) (046.11)
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