ICD-9-CM

Excludes:

hepatolenticular degeneration (275.1)

multiple sclerosis (340)

other demyelinating diseases of central nervous system (341.0-341.9)

330 Cerebral degenerations usually manifest in childhood Use additional code to identify associated intellectual disabilities
330.0: Leukodystrophy Krabbe's disease Leukodystrophy: NOS globoid cell metachromatic sudanophilic Pelizaeus-Merzbacher disease Sulfatide lipidosis
330.1: Cerebral lipidoses Amaurotic (familial) idiocy Disease: Batten Jansky-Bielschowsky Kufs' Spielmeyer-Vogt Tay-Sachs Gangliosidosis
330.2: Cerebral degeneration in generalized lipidoses Code first underlying disease, as: Fabry's disease (272.7) Gaucher's disease (272.7) Niemann-Pick disease (272.7) sphingolipidosis (272.7)
330.3: Cerebral degeneration of childhood in other diseases classified elsewhere Code first underlying disease, as: Hunter's disease (277.5) mucopolysaccharidosis (277.5)
330.8: Other specified cerebral degenerations in childhood Alpers' disease or gray-matter degeneration Infantile necrotizing encephalomyelopathy Leigh's disease Subacute necrotizing encephalopathy or encephalomyelopathy
330.9: Unspecified cerebral degeneration in childhood

330 Cerebral degenerations usually manifest in childhood

Use additional code to identify associated intellectual disabilities

Krabbe's disease

Leukodystrophy:

NOS

globoid cell

metachromatic

sudanophilic

Pelizaeus-Merzbacher disease

Sulfatide lipidosis