HEREDITARY AND DEGENERATIVE DISEASES OF THE CENTRAL NERVOUS SYSTEM (330-337)
Excludes:
hepatolenticular degeneration (275.1)
multiple sclerosis (340)
other demyelinating diseases of central nervous system (341.0-341.9)
331 Other cerebral degenerations
Use additional code, where applicable, to identify dementia:
with behavioral disturbance (294.11)
without behavioral disturbance (294.10)
331.0: Alzheimer's disease
331.1: Frontotemporal dementia
331.2: Senile degeneration of brain
Excludes:
senility NOS (797)
331.3: Communicating hydrocephalus
Secondary normal pressure hydrocephalus
Excludes:
congenital hydrocephalus (742.3)
idiopathic normal pressure hydrocephalus (331.5)
normal pressure hydrocephalus (331.5)
spina bifida with hydrocephalus (741.0)
331.4: Obstructive hydrocephalus
Acquired hydrocephalus NOS
Excludes:
congenital hydrocephalus (742.3)
idiopathic normal pressure hydrocephalus (331.5)
normal pressure hydrocephalus (331.5)
spina bifida with hydrocephalus (741.0)
331.5: Idiopathic normal pressure hydrocephalus (INPH)
Normal pressure hydrocephalus NOS
Excludes:
congenital hydrocephalus (742.3)
secondary normal pressure hydrocephalus (331.3)
spina bifida with hydrocephalus (741.0)
331.6: Corticobasal degeneration
331.7: Cerebral degeneration in diseases classified elsewhere
Code first underlying disease, as:
alcoholism (303.0-303.9)
beriberi (265.0)
cerebrovascular disease (430-438)
congenital hydrocephalus (741.0, 742.3)
neoplastic disease (140.0-239.9)
myxedema (244.0-244.9)
vitamin B12 deficiency (266.2)
Excludes:
cerebral degeneration in:
Jakob-Creutzfeldt disease (046.11-046.19)
progressive multifocal leukoencephalopathy (046.3)
subacute spongiform encephalopathy (046.1)
331.8: Other cerebral degeneration
331.9: Cerebral degeneration, unspecified

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