Endocrine, nutritional and metabolic diseases (E00-E89)
Metabolic disorders (E70-E88)

excludes1
androgen insensitivity syndrome (E34.5-)
congenital adrenal hyperplasia (E25.0)
hemolytic anemias attributable to enzyme disorders (D55.-)
Marfan's syndrome (Q87.4)
5-alpha-reductase deficiency (E29.1)

excludes2
Ehlers-Danlos syndromes (Q79.6-)
E70: Disorders of aromatic amino-acid metabolism
E71: Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
E72: Other disorders of amino-acid metabolism
E73: Lactose intolerance
E74: Other disorders of carbohydrate metabolism
E75: Disorders of sphingolipid metabolism and other lipid storage disorders
E76: Disorders of glycosaminoglycan metabolism
E77: Disorders of glycoprotein metabolism
E78: Disorders of lipoprotein metabolism and other lipidemias
E79: Disorders of purine and pyrimidine metabolism
E80: Disorders of porphyrin and bilirubin metabolism
E83: Disorders of mineral metabolism
E84: Cystic fibrosis
E85: Amyloidosis
E86: Volume depletion
E87: Other disorders of fluid, electrolyte and acid-base balance
E88: Other and unspecified metabolic disorders

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