282: Hereditary hemolytic anemias
282.4 Thalassemias
Excludes:
sickle-cell:
disease (282.60-282.69)
trait (282.5)
282.40: Thalassemia, unspecified
Thalassemia NOS
282.41: Sickle-cell thalassemia without crisis
Microdrepanocytosis
Sickle-cell thalassemia NOS
Thalassemia Hb-S disease without crisis
282.42: Sickle-cell thalassemia with crisis
Sickle-cell thalassemia with vaso-occlusive pain
Thalassemia Hb-S disease with crisis
Use additional code for type of crisis, such as:
Acute chest syndrome (517.3)
Splenic sequestration (289.52)
282.43: Alpha thalassemia
Alpha thalassemia major
Hemoglobin H Constant Spring
Hemoglobin H disease
Hydrops fetalis due to alpha thalassemia
Severe alpha thalassemia
Triple gene defect alpha thalassemia
Excludes:
alpha thalassemia trait or minor (282.46)
hydrops fetalis due to isoimmunization (773.3)
hydrops fetalis not due to immune hemolysis (778.0)
282.44: Beta thalassemia
Beta thalassemia major
Cooley's anemia
Homozygous beta thalassemia
Severe beta thalassemia
Thalassemia intermedia
Thalassemia major
Excludes:
beta thalassemia minor (282.46)
beta thalassemia trait (282.46)
delta-beta thalassemia (282.45)
hemoglobin E beta thalassemia (282.47)
sickle-cell beta thalassemia (282.41, 282.42)
282.45: Delta-beta thalassemia
Homozygous delta-beta thalassemia
Excludes:
delta-beta thalassemia trait (282.46)
282.46: Thalassemia minor
Alpha thalassemia minor
Alpha thalassemia silent carrier
Alpha thalassemia trait
Beta thalassemia minor
Beta thalassemia trait
Delta-beta thalassemia trait
Thalassemia trait NOS
Excludes:
alpha thalassemia (282.43)
beta thalassemia (282.44)
delta-beta thalassemia (282.45)
hemoglobin E-beta thalassemia (282.47)
sickle-cell trait (282.5)
282.47: Hemoglobin E-beta thalassemia
Excludes:
beta thalassemia (282.44)
beta thalassemia minor (282.46)
beta thalassemia trait (282.46)
delta-beta thalassemia (282.45)
delta-beta thalassemia trait (282.46)
hemoglobin E disease (282.7)
other hemoglobinopathies (282.7)
sickle-cell beta thalassemia (282.41, 282.42)
282.49: Other thalassemia
Dominant thalassemia
Hemoglobin C thalassemia
Hereditary leptocytosis
Mediterranean anemia (with other hemoglobinopathy)
Mixed thalassemia
Thalassemia with other hemoglobinopathy
Excludes:
hemoglobin C disease (282.7)
hemoglobin E disease (282.7)
other hemoglobinopathies (282.7)
sickle-cell anemias (282.60-282.69)
sickle-cell beta thalassemia (282.41-282.42)

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